Título : |
Nephrotic syndrome associated with primary atypical hemolytic uremic syndrome |
Tipo de documento : |
documento electrónico |
Autores : |
John Fredy Nieto Ríos, |
Fecha de publicación : |
2020 |
Títulos uniformes : |
Brazilian Journal of Nephrology
|
Idioma : |
Inglés (eng) |
Palabras clave : |
Atypical Hemolytic Uremic Syndrome Nephrotic Syndrome Acute Renal Injury Hypertension Complement System Proteins |
Resumen : |
Primary atypical hemolytic-uremic syndrome is a rare disease characterized by non-immune microangiopathic hemolytic anemia, thrombocytopenia, and renal dysfunction; it is related to alterations in the regulation of the alternative pathway of complement due to genetic mutations. The association with nephrotic syndrome is unusual. We present here a pediatric patient diagnosed with primary atypical hemolytic-uremic syndrome associated with nephrotic syndrome who responded to eculizumab treatment. |
Mención de responsabilidad : |
Diana Carolina Bello-Marquez, John Fredy Nieto-Rios, Lina Maria Serna-Higuita, Alfonso Jose Gonzalez-Vergara |
Referencia : |
J Bras Nefrol. Jul-Sep 2021;43(3):440-444. |
DOI (Digital Object Identifier) : |
10.1590/2175-8239-jbn-2020-0050 |
PMID : |
32779691 |
Derechos de uso : |
CC BY |
En línea : |
https://bjnephrology.org/en/article/nephrotic-syndrome-associated-with-primary-a [...] |
Enlace permanente : |
https://hospitalpablotobon.cloudbiteca.com/pmb/opac_css/index.php?lvl=notice_dis |