Nephrotic syndrome associated with primary atypical hemolytic uremic syndrome [documento electrónico] / John Fredy Nieto Ríos,  . - 2020.
Obra : Brazilian Journal of Nephrology

Idioma : Inglés (eng)

Palabras clave :	Atypical Hemolytic Uremic Syndrome  Nephrotic Syndrome  Acute Renal Injury  Hypertension  Complement System Proteins
Resumen :	Primary atypical hemolytic-uremic syndrome is a rare disease characterized by non-immune microangiopathic hemolytic anemia, thrombocytopenia, and renal dysfunction; it is related to alterations in the regulation of the alternative pathway of complement due to genetic mutations. The association with nephrotic syndrome is unusual. We present here a pediatric patient diagnosed with primary atypical hemolytic-uremic syndrome associated with nephrotic syndrome who responded to eculizumab treatment.
Mención de responsabilidad :	Diana Carolina Bello-Marquez, John Fredy Nieto-Rios, Lina Maria Serna-Higuita, Alfonso Jose Gonzalez-Vergara
Referencia :	J Bras Nefrol. Jul-Sep 2021;43(3):440-444.
DOI (Digital Object Identifier) :	10.1590/2175-8239-jbn-2020-0050
PMID :	32779691
Derechos de uso :	CC BY
En línea :	https://bjnephrology.org/en/article/nephrotic-syndrome-associated-with-primary-a [...]
Enlace permanente :	https://hospitalpablotobon.cloudbiteca.com/pmb/opac_css/index.php?lvl=notice_display&id=5738