Título : |
Malignant peripheral nerve sheath tumor in a child |
Tipo de documento : |
documento electrónico |
Autores : |
Lina Marcela Cadavid Álvarez, ; Gabriel Jaime Varela Aguirre, |
Fecha de publicación : |
2021 |
Títulos uniformes : |
Radiology Case Reports
|
Idioma : |
Inglés (eng) |
Palabras clave : |
Child Malignant peripheral nerve sheath tumor Nerve sheath neoplasms Neurofibroma Peripheral nerve Schwannoma |
Resumen : |
Among the diverse causes of posterior mediastinal masses, malignant peripheral nerve sheath tumors is a very rare neurogenic tumor. Imaging features tend to be variable. A 20-month-old toddler presented with a 3-month history of persistent diffuse thoracic and abdominal pain. A chest magnetic resonance imaging was taken and shown a posterior mediastinal lesion. Histopathology and immunohistochemical analysis confirmed the diagnosis of a malignant peripheral nerve sheath tumor with myxoid areas. Malignant peripheral nerve sheath tumors are an uncommon entity in the children with a poor prognosis. Magnetic resonance imaging is the preferred technique in children to limit the use of ionizing radiation and because has a higher contrast resolution; however, all suspicious tumors should be biopsied to make an appropriate diagnosis. Treatment is radical surgery with excision of the entire mass; however, there is a high incidence of local recurrence. |
Mención de responsabilidad : |
Brian Daniel Noreña-Rengifo MD, Lina Marcela Cadavid-Alvarez RR, Patricia Eugenia Gil-Serrano RR y Gabriel Jaime Varela-Aguirre PR |
Referencia : |
Radiol Case Rep. 2020 Nov 12;16(1):145-151. |
DOI (Digital Object Identifier) : |
10.1016/j.radcr.2020.10.028 |
PMID : |
33224401 |
Derechos de uso : |
CC BY-NC-ND |
En línea : |
https://linkinghub.elsevier.com/retrieve/pii/S1930-0433(20)30547-1 |
Enlace permanente : |
https://hospitalpablotobon.cloudbiteca.com/pmb/opac_css/index.php?lvl=notice_dis |