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Primitive neuroectodermal tumor of the liver: a case report of a rare case in pediatrics / Lina Marcela Cadavid Álvarez ; Jorge Alberto Ochoa Gaviria ; Juan Camilo Pérez Cadavid
Título : Primitive neuroectodermal tumor of the liver: a case report of a rare case in pediatrics Tipo de documento : documento electrónico Autores : Lina Marcela Cadavid Álvarez, ; Jorge Alberto Ochoa Gaviria, ; Juan Camilo Pérez Cadavid, Fecha de publicación : 2021 Títulos uniformes : Radiology Case Reports Idioma : Inglés (eng) Palabras clave : Primitive neuroectodermal tumor Focal hepatic lesion Ewing sarcoma Resumen : Primitive neuroectodermal tumors (PNETs) belong to the Ewing sarcoma family of tumors. These lesions are highly aggressive and are usually found in paravertebral regions, lower limbs, and thorax. However, abdominal PNETs are extremely rare, and only 3 cases of pediatric PNET of the liver have been previously reported. Most patients exhibit symptoms associated with mass effect, due to rapid tumor growth and dissemination. Therefore, an appropriate differential diagnosis is of pivotal importance in order to initiate the corresponding treatment. Here we report the case of a 4-year-old female patient who was diagnosed with PNET of the liver, and we discuss the analysis of focal liver lesions and differential diagnosis in pediatric patients. Mención de responsabilidad : Juan David Vásquez Montoya, Lina Marcela Cadavid Álvarez, Jorge Alberto Ochoa Gaviria, Juan Camilo Pérez Cadavid Referencia : Radiol Case Rep. 2021 Jun 13;16(8):2220-2225. DOI (Digital Object Identifier) : 10.1016/j.radcr.2021.05.001 PMID : 34178196 Derechos de uso : CC BY-NC-ND En línea : https://linkinghub.elsevier.com/retrieve/pii/S1930043321002909 Enlace permanente : https://hospitalpablotobon.cloudbiteca.com/pmb/opac_css/index.php?lvl=notice_display&id=5803 Primitive neuroectodermal tumor of the liver: a case report of a rare case in pediatrics [documento electrónico] / Lina Marcela Cadavid Álvarez, ; Jorge Alberto Ochoa Gaviria, ; Juan Camilo Pérez Cadavid, . - 2021.
Obra : Radiology Case Reports
Idioma : Inglés (eng)
Palabras clave : Primitive neuroectodermal tumor Focal hepatic lesion Ewing sarcoma Resumen : Primitive neuroectodermal tumors (PNETs) belong to the Ewing sarcoma family of tumors. These lesions are highly aggressive and are usually found in paravertebral regions, lower limbs, and thorax. However, abdominal PNETs are extremely rare, and only 3 cases of pediatric PNET of the liver have been previously reported. Most patients exhibit symptoms associated with mass effect, due to rapid tumor growth and dissemination. Therefore, an appropriate differential diagnosis is of pivotal importance in order to initiate the corresponding treatment. Here we report the case of a 4-year-old female patient who was diagnosed with PNET of the liver, and we discuss the analysis of focal liver lesions and differential diagnosis in pediatric patients. Mención de responsabilidad : Juan David Vásquez Montoya, Lina Marcela Cadavid Álvarez, Jorge Alberto Ochoa Gaviria, Juan Camilo Pérez Cadavid Referencia : Radiol Case Rep. 2021 Jun 13;16(8):2220-2225. DOI (Digital Object Identifier) : 10.1016/j.radcr.2021.05.001 PMID : 34178196 Derechos de uso : CC BY-NC-ND En línea : https://linkinghub.elsevier.com/retrieve/pii/S1930043321002909 Enlace permanente : https://hospitalpablotobon.cloudbiteca.com/pmb/opac_css/index.php?lvl=notice_display&id=5803 Reserva
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